Insuffisance surrénale aiguë. Authors; Authors and affiliations. Aude Mariani Ecochard. Aude Mariani Ecochard. There are no affiliations available. Chapter. l’insuffisance surrénale aiguë. Jérôme Bertherat, Paris. 10hh Diagnostic de l’insuffisance surrénale: facile ou difficile? Antoine Tabarin, Bordeaux. Request PDF on ResearchGate | On Oct 1, , M. Molimard and others published Insuffisance surrénalienne aiguë et hypercorticisme induits par des.
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Acute adrenal insufficiency AAI is a rare but severe condition caused by a sudden defective production of adrenal steroids cortisol and aldosterone.
Summary Epidemiology Exact prevalence of acute adrenal insufficiency is unknown. Diagnostic methods The clinical signs are nonspecific but the diagnosis of AAI is suspected if a patient presents with hypotonia or shock that responds poorly to catecholamines.
Peritonitis is often a differential diagnosis as well as other causes of adrenal destruction such as bilateral adrenalectomy, Waterhouse-Friderichsen syndrome see this termautoimmune adrenalitis, infectious adrenalitis and tumour infiltration.
Acute adrenal failure Acute adrenocortical insufficiency Addisonian crisis Adrenal crisis Adrenocortical crisis Prevalence: Adrenal destruction may be associated with autoimmune adrenalitis Addison disease; see this termisolated or in the context of autoimmune polyendocrinopathy type 1, 2 or 4 see these terms. The disease may occur at any age. Health care resources for this disease Expert centres Diagnostic tests 0 Patient organisations 5 Orphan drug s 4.
Orphanet: Insuffisance surrenalienne aigue
Administration of mg hydrocortisone i. Summary and related texts. The documents contained in this web site are presented for information purposes only. The initial presentation may be limited to abdominal pain, nausea, vomiting and fever. Disease definition Acute adrenal insufficiency AAI is a rare but severe condition caused by a sudden defective production of adrenal steroids cortisol and aldosterone.
The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.
Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. Only comments written in English can be processed. Secondary adrenal insufficiency needs to be eliminated.
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Etiology Steroid withdrawal is the most common cause of AAI in patients with chronic adrenal insufficiency. The clinical signs are nonspecific but the diagnosis of AAI is suspected if a patient presents with hypotonia or shock that responds poorly to catecholamines.
Prognosis varies depending on the etiologies, but is generally correlated with the rapidity of diagnosis and medical assistance. If aigie, shock and bilateral adrenal hemorrhage can rapidly lead to death.
For all other comments, please send your remarks via contact us. Differential diagnosis Secondary adrenal insufficiency needs to be eliminated. Immediate treatment in an intensive care unit is necessary. Antibiotics, vasopressors, heparin, packed red blood cells, skrrenalienne, cryoprecipitates and fresh frozen plasma are also administered if needed.
Death is rare when the patients receive appropriate medical assistance.
Affections surrénaliennes aiguës – EM|consulte
The mineralocorticoid insufficiency, when present, can be confirmed by low aldosterone levels and high plasma renin activity PRA. It represents an emergency, thus the rapid recognition and prompt therapy are critical for survival even before the diagnosis is made. The onset is often sudden. Preventive strategies include dosage increase of steroid hormones during times of stress in those with CPIA. AAI may also result insuffisqnce corticotroph insufficiency, either isolated or more often resulting from complete anterior pituitary insufficiency.
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Specialised Social Services Eurordis directory. Prognosis Prognosis varies depending on the etiologies, but is surrenzlienne correlated with the rapidity of diagnosis and medical assistance. Other search option s Alphabetical list.